The imaging of the aortic fibrous membrane associated with Williams syndrome/Williams sendromu ile iliskili aortik fibroz membran goruntusu.
A 20-year-old woman was admitted for evaluation of her cardiac murmur. She was short in stature, had a characteristic face of WS and moderate mental retardation, whereas she was talkative and gregarious. On auscultation, a harsh systolic murmur that radiated to the bilateral neck vessels on the second sternal border was audible. The electrocardiogram revealed left ventricular hypertrophy, and chest radiography showed no abnormality. The transthoracic echocardiography detected no aortic valve or left ventricular outflow tract obstruction, however, there was 143 mmHg pressure gradient at the aortic level with Doppler echocardiography (Fig. 1A). On the suprasternal echocardiographic view (Fig 1A) and the aortogram (Fig. 1B and 1C, Video 1. See corresponding video/movie images at www.anakarder.com), a discrete fibrous membrane above sinuses of Valsalva was seen. The discrete fibrous membrane was confirmed at surgery, and aortoplasty for supravalvular aortic stenosis was performed successfully.
[FIGURE 1 OMITTED]
Haci Ciftci, Ozcan Ozeke (1), Fikri Kutlay *, Ugur Yuvanc (2)
From Departments of Cardiology and * Cardiovascular Surgery, Veni Vidi Hospital; (1) Department of Cardiology, Diyarbakir Military Hospital; (2) Department of Cardiology, Guneydogu Hospital, Diyarbakir, Turkey
Address for Correspondence/Yazisma Adresi: Ozcan Ozeke, MD Diyarbakir Asker Hastanesi Kardiyoloji Klinigi Diyarbakir, Turkey Mobile:+90 505 383 67 73 E-mail: email@example.com
|Printer friendly Cite/link Email Feedback|
|Title Annotation:||E-page Original Images/E-sayfa Orijinal Goruntuler|
|Author:||Ciftci, Haci; Ozeke, Ozcan; Kutlay, Fikri; Yuvanc, Ugur|
|Publication:||The Anatolian Journal of Cardiology (Anadolu Kardiyoloji Dergisi)|
|Article Type:||Case study|
|Date:||Apr 1, 2008|
|Previous Article:||Thrombotic lesion of saphenous vein graft resolved by antiaggregant therapy/ Antiagregan tedavi ile cozulen trombotik safen ven grefti lezyonu.|
|Next Article:||A rare radiodiagnostic finding: totally and severely calcified aorta-the Porcelain aorta/Nadir bir radyodiyagnostik bulgu: butunuyle ve ciddi sekilde...|