Flexion-Induced Cervical Cord Compression: Hirayama Disease.
Hirayama disease is a rare self-limited condition characterized by asymmetric muscle weakness and amyotrophy of the distal upper limbs involving the C7-T1 myotomes. The pathologic findings implicate circulatory changes in the lower cervical cord, which causes ischemic changes in the anterior horn. Congestion of the venous plexus, abnormal drainage in the vertebral venous plexus, or malformation of the epidural vessels may be responsible (1,2). In this case, the diagnosis is guided mainly by electrophysiological and flexion magnetic resonance imaging findings.
Conflict of Interest: No conflict of interest was declared by the authors.
(1.) Hirayama K. Juvenile muscular atrophy of distal upper extremity (Hirayama disease). Intern Med 2000;39:283-90.
(2.) Lyu RK, Huang YC, Wu YR, Kuo HC, Ro LS, Chen CM, et al. Electrophysiological features of Hirayama disease. Muscle Nerve 2011;44:185-90.
Sena Tolu (1), Fikret Aysal (2), Tugrul Ormeci (3), Ibrahim Ethem Kirez (1), Nurbanu Hindioglu (1)
(1) Department of Physical Medicine and Rehabilitation, Medipol University School of Medicine, Istanbul, Turkey
(2) Department of Neurology, Medipol University School of Medicine, Istanbul, Turkey
(3) Department of Radiology, Medipol University School of Medicine, Istanbul, Turkey
Address for Correspondence: Sena Tolu, Department of Physical Medicine and Rehabilitation, Medipol University School of Medicine, Istanbul, Turkey
Phone: +90 505 442 47 22
Received: 5 January 2019
Accepted: 20 February 2019
Available at www.balkanmedicaljournal.org
Cite this article as:
Tolu S, Aysal F, Ormeci T, Kirez IE, Hindioglu N. Flexion-Induced Cervical Cord Compression: Hirayama Disease. Balkan Med J 2019;36:190-1
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|Title Annotation:||Clinical Image|
|Author:||Tolu, Sena; Aysal, Fikret; Ormeci, Tugrul; Kirez, Ibrahim Ethem; Hindioglu, Nurbanu|
|Publication:||Balkan Medical Journal|
|Date:||May 1, 2019|
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